Case Reports

Fahr’s syndrome: a rare case report

Edwin Sridana , Suprayoga Sukmana Putra

Edwin Sridana
Badung Regency Mangusada Hospital, Bali, Indonesia. Email: edwin123@yahoo.com

Suprayoga Sukmana Putra
Badung Regency Mangusada Hospital, Bali, Indonesia
Online First: December 15, 2016 | Cite this Article
Sridana, E., Putra, S. 2016. Fahr’s syndrome: a rare case report. Indonesia Journal of Biomedical Science 10(2): 15-19. DOI:10.15562/ijbs.v10i2.125


Fahr’s syndrome is a rare neurodegenerative disorder characterized by bilateral basal ganglia calcification. The exact incidence of Fahr’s syndrome is still unknown but estimated to be <1/1,000,000. On routine non-contrast-CT scan examination, 0.3-1.2% cases of intracranial calcification can be incidentally detected. It is caused by several medical conditions, with hypothyroidism as the most common one. Patient may come with neurologic or psychiatric symptoms. CT scan is the main supportive examination; it is used to determine the location and extension of calcification. Therapy is directed to the underlying etiology and usually symptomatic. A female, 46 years old, came with stiffness on both hands. This symptom appeared multiple times during past decade but with mild intensity. CT scan revealed calcification in both cerebral hemisphere and cerebellum. Blood test showed low calcium concentration. Patient was diagnosed with Fahr’s syndrome and given anticonvulsant and calcium supplementation. She was getting better during hospitalization and then discharged 4 days later with oral home medication.

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