Background: Hypoparathyroid is an endocrine disorder that is characterized by hypocalcemia and hyperphosphatemia due to insufficient secretion of parathyroid hormone. Mostly, this disease is secondary caused by neck surgery and it is responsible for almost all cases of hypoparathyroid. Parathyroid hormones responsibles for maintaining homeostasis of calcium. Fahr syndrome is a neurodegenerative disorder characterized by bilateral basal ganglia calcification that is caused by endocrine disorder such as hypoparathyroid.
Case Presentation: In this case report, we reported a 70 years old woman with secondary hypoparathyroidism presenting with Fahr's syndrome after total thyroidectomy. Besides hypocalcemia and hyperphosphatemia as signs of secondary hypoparathyroidism, specific clinical signs with Fahr's syndrome in this case is presence of multiple calcifications in several parts of the brain and specifically in the bilateral of basal ganglia. Management of this disease mainly focused on supplementation of calcium and vitamin D.
Conclusion: Fahr syndrome is a rare, genetically dominant, inherited neurological disorder that should be considered as the main problem in several patients with post total thyroidectomy.